ATP-dependent Lon protease; involved in degradation of misfolded proteins in mitochondria; required for biogenesis and maintenance of mitochondria [Source:SGD;Acc:S000000118]
LON1
Chromosome II: 177,874-181,275 reverse strand.
R64-1-1:BK006936.2
This gene has 1 transcript (splice variant), 387 orthologues and is a member of 2 Ensembl protein families.