Catalytic subunit of i-AAA protease complex; complex is located in mitochondrial inner membrane; responsible for degradation of unfolded or misfolded mitochondrial gene products; serves as nonconventional translocation motor to pull PNPase into intermembrane space; also has role in intermembrane space protein folding; mutation causes elevated rate of mitochondrial turnover; human homolog YME1L1 can complement yeast null mutant [Source:SGD;Acc:S000006228]

OSD1, YTA11

Chromosome XVI: 610,481-612,724 forward strand.

R64-1-1:BK006949.2

This gene has 1 transcript (splice variant), 339 orthologues, 2 paralogues and is a member of 2 Ensembl protein families.

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