tRNA-specific 2-thiouridylase; responsible for 2-thiolation of the wobble base of mitochondrial tRNAs; human homolog TRMU is implicated in myoclonus epilepsy associated with ragged red fibers (MERRF), and can complement yeast null mutant [Source:SGD;Acc:S000002191]

MTO2, MTU1

Chromosome IV: 392,659-393,912 reverse strand.

R64-1-1:BK006938.2

This gene has 1 transcript (splice variant), 171 orthologues and is a member of 1 Ensembl protein family.

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