Flavin-dependent monooxygenase involved in ubiquinone biosynthesis; responsible for hydroxylation at position C5 and deamination at C4 during ubiquinone (Coenzyme Q) biosynthesis; localizes to matrix face of mitochondrial inner membrane in a large complex with other ubiquinone biosynthetic enzymes; human homolog COQ6 can complement yeast null mutant and is implicated in steroid-resistant nephrotic syndrome (SRNS) [Source:SGD;Acc:S000003487]
Chromosome VII: 1,002,523-1,003,962 reverse strand.
This transcript has 1 exon, is annotated with 17 domains and features, is associated with 33 variant alleles and maps to 29 oligo probes.
This transcript is a product of gene YGR255C Show transcript tableHide transcript table